JCIH 2007 Position Statement Risk Factors

The Joint Committee on Infant Hearing (JCIH) recommends in the JCIH Position Statement 2007 that infants who have a risk factor for late onset hearing loss should have at least one comprehensive audiologic evaluation by 24 to 30 months of age. Testing should also occur any time there is parent, caregiver or professional concern regarding communication development. 

Here is a list of the JCIH 2007 Risk Indicators Associated with Congenital, Delayed-Onset, or Progressive Hearing Loss in Childhood:

(* Indicates risk indicators are of greater concern for delayed onset hearing loss): 

  • Parent or caregiver concern* regarding hearing, speech, language or developmental delay.
  • Family history* of permanent childhood hearing loss.
  • Neonatal intensive care of >5 days, which may include extracorporeal membrane oxygenation* (ECMO) assisted ventilation, exposure to ototoxic medications (gentamicin and tobramycin) or loop diuretics (furosemide/lasix), and hyperbilirubinemia requiring exchange transfusion.
  • In-utero infections such as cytomegalovirus*, herpes, rubella, syphilis, and toxoplasmosis.
  • Craniofacial anomalies, including those involving the pinna, ear canal, ear tags, ear pits, and temporal bone anomalies.
  • Physical findings such as white forelock, associated with a syndrome known to include sensorineural or permanent conductive hearing loss.
  • Syndromes associated with hearing loss or progressive or late onset hearing loss* such as neurofibromatosis, osteopetrosis, and Usher syndrome. Other frequently identified syndromes include Waardenburg, Alport, Pendred, and Jervell and Lange-Nielson.
  • Neurodegenerative disorders*, such as Hunter syndrome, or sensory motor neuropathies, such as Friedreich's ataxia and Charcot-Marie-Tooth syndrome.
  • Culture positive postnatal infections associated with sensorineural hearing loss*, including confirmed bacterial and viral (especially herpes and varicella) meningitis.
  • Head trauma, especially basal skull/temporal bone fracture* requiring hospitalization.
  • Chemotherapy*.